원발성 국한성 후두 기관기관지형 유전분증 1예 (A Case of Primary Localized Laryngo-tracheobronchial Amyloidosis)

서지정보

· 발행기관 : 대한결핵및호흡기학회
· 수록지 정보 : Tuberculosis and Respiratory Diseases / 65권 / 6호 / 532 ~ 536페이지
· 저자명 : 이석정, 리원연, 정순희, 권우철, 이선녕, 이남석, 김상하, 신계철, 용석중

초록

저자들은 가래를 동반한 기침과 쉰 목소리로 내원한 68세 남자에게 흉부 전산화 단층촬영으로 우중엽 무기폐를 확인하고 기관지경 및 생검을 시행하여 후두와 기관기관지에 국한된 유전분증 1예를 경험하였기에 문헌고찰과 함께 보고한다.

영어초록

We report on a case of a patient with laryngo-tracheobronchial amyloidosis who complained of cough, sputum,and hoarseness. A chest X-ray showed consolidation in the right middle lobe. A chest CT scan showed diffuse,irregular narrowing of the tracheobronchial tree and atelectasis of the right middle lobe, with calcification of bronchial wall. Bronchoscopic findings were multinodular submucosal thickening of the right vocal cord, and yellowish multinodular submucosal thickening from the lower trachea through both main bronchi, as well as the
lingular division of the left upper lobe, the right middle lobe, and the right lower lobe. The right middle lobe bronchus was nearly obstructed. The diagnosis of amyloidosis was made by multiple bronchoscopic biopsies on the right vocal cord and both bronchi. Pathologic findings were characteristic apple-green birefringence under polarized microscopy with Congo-red stain. The patient had no evidence of systemic amyloidosis. The patient is under conservative symptomatic treatment

참고자료

· 없음