기저세포모반증후군과 연관된 다발성 치성각화낭종의 치료시 술전 조대술과 술후 교정적 맹출의 사용 치험 1례 (CASE REPORT OF TREATMENT OF MULTIPLE ODONTOGENIC KERATOCYSTS WITH BASAL CELL NEVUS SYNDROME USING PREOPERATIVE MARSUPIALIZATION AND ORTHODONTIC EXTRUSION)

서지정보

· 발행기관 : 대한악안면성형재건외과학회
· 수록지 정보 : Maxillofacial Plastic Reconstructive Surgery / 31권 / 5호 / 429 ~ 434페이지
· 저자명 : 강태인, 박영주, 남정훈, 안장훈, 송준호, 신진업, 정재안, 강혜진

초록

Basal cell nevus syndrome is a rare inherited disorder characterized by mulitple cutaneous basal cell carcinoma,
pits of the palms and soles, cysts of the jaws, skeletal abnormalities and ectopic calcifications.
Currently there are new lines of investigation based on biomolecular studies, which aim at identifying the
molecules responsible for these cysts and thus early allowing an early diagnosis of these patients.
We report a case of a 9-year-old boy with the various manifestation of basal cell nevus syndrome, which
are multiple odontogenic keratocysts, pits of the soles, bifid ribs, ectopic calcification, macrocephaly, and
hypertelorism, etc. Total five odontogenic keratocysts were found. For the reduction of the size of the odontogenic
keratocysts, following preoperative marsupialization, there were surgically enucleated. And the
impacted upper right lateral incisor and canine are tracted orthodontically.

영어초록

Basal cell nevus syndrome is a rare inherited disorder characterized by mulitple cutaneous basal cell carcinoma,
pits of the palms and soles, cysts of the jaws, skeletal abnormalities and ectopic calcifications.
Currently there are new lines of investigation based on biomolecular studies, which aim at identifying the
molecules responsible for these cysts and thus early allowing an early diagnosis of these patients.
We report a case of a 9-year-old boy with the various manifestation of basal cell nevus syndrome, which
are multiple odontogenic keratocysts, pits of the soles, bifid ribs, ectopic calcification, macrocephaly, and
hypertelorism, etc. Total five odontogenic keratocysts were found. For the reduction of the size of the odontogenic
keratocysts, following preoperative marsupialization, there were surgically enucleated. And the
impacted upper right lateral incisor and canine are tracted orthodontically.

참고자료

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