vacteri syndrome. imperforate anus [PPT] case study

소개글

vacteri syndrome.
imperforate anus
에 대한 케이스 스터디였으나 간호진단중재는 없습니다.
의사 컨퍼런스 발표자료로 사용되었으며 심도있는 자료가 될것입니다.
발표자료로 괜찮다고 생각합니다.
[PPT]

목차

Present illness
History
Review of System
Physical Examination
Laboratory Finding
Problem List
Initial Plan
초음파/CT영상
Imperforate anus
VACTERL syndrome
eatment

본문내용

VACTERL syndrome

Definition
A nonrandom association of birth defects.
Diagnosis can be with at least 3 of the defects
V = Vertebral anomalies; and
A = Anal atresia (no hole at the bottom end of the intestine);
C = Cardiac defect, most often ventricular septal defect;
TE = TracheoEsophageal fistula (communication between the esophagus and trachea) with esophageal atresia (part of the esophagus is not hollow);
R = Renal (kidney) abnormalities; and
L = Limb abnormalities, most often radial dysplasia (abnormal formation of the thumb or the radius bone in the forearm).

Prenatal USG finding
Multi organ anomaly
IUGR
Small stomach
Hydramnion
One cord atery

Epidemiology
The VACTERL association has an estimated incidence of 16 cases per 100,000 live births.
It is seen more frequently in infants born to diabetic mothers.
Estroprogestins, methimazole, doxorubicin drug Hx
Genetic linkage
VACTERAL -H : 수두증동반
David-Ocallaghan : 상염색체 열성
Hunter-MacMurray: x-연관 열성

Treatment
Operation of each anomaly ( M/C)
motality : 정상 신생아보다 25배
complication after op : esophagus atresia, stenosis,
fistula recur, GERD

참고 자료

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